PFapa with facial swelling- A new association?

B. Khodaghalian, K. K. Tewary, H. Narchi

Research output: Contribution to journalArticlepeer-review

1 Citation (Scopus)


PFAPA (periodic fever, apthous stomatitis, pharyngitis, cervical adenitis) is a rare condition of unknown cause affecting children. Although the exact etiology is unknown, inflammatory, immunological or genetic causes have been suggested. The diagnosis is made by exclusion of other causes of periodic fever. Although management is essentially symptomatic, single corticosteroid dose, tonsillectomy and Cimetidine has been shown to be associated with resolution of symptoms. Although abdominal pain and genital ulcers have been reported in association with PFAPA, unilateral transient facial swelling has not been previously reported. The authors present a hitherto unreported association of PFAPA with recurrent episodes of unilateral facial swelling.

Original languageEnglish
Pages (from-to)425-427
Number of pages3
JournalIndian Journal of Pediatrics
Issue number5
Publication statusPublished - May 2013


  • Facial swelling
  • Pediatrics
  • Periodic fever
  • Syndrome

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health


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